Atlantoaxial Instability

Associations

  • Morquios
  • Spondyloepiphyseal dysplasia
  • Achondroplasia
  • Downs- 25% have instability
  • Pharyngeal infection in the normal child (= Grisels syndrome)- due to hyperaemia causing demineralisation of the attachment of the transverse ligament to the anterior arch of the atlas
  • rotatory subluxation or anterior subluxation

Atlanto Dens Interval

  • more than 5mm = instability
  • more than10mm = indication for surgery

Reviewed by Professor Phong Tran, Head of Orthopaedic Surgery, Western Health. Last updated 10 October 2026.