Genetic Disorders, Skeletal Dysplasias & Malformations
Eosinophilic Granuloma
- Bone lesion with lipid laden histiocytes
- Look like tennis racket cell in bet eosinophils
- Litterer – Siwe
- Fulminant & death by 2 months
- Hans – Shuler – Christian
- Diabeties insipidous
- Pancytopenia
- Skull involvement

